Cervical artery dissection: An atypical presentation with Ehlers-Danlos-like collagen pathology?

نویسندگان

  • D Ulbricht
  • N J Diederich
  • T Hermanns-Lê
  • R J Metz
  • F Macian
  • G E Piérard
چکیده

The authors took skin biopsies of the macroscopically normal skin of seven consecutive patients with spontaneous cervical artery dissection (SCAD). Histologically, alterations of the collagen and elastic fiber networks were found in six patients. In five, the histologic, immunohistochemical, and ultrastructural changes were similar to those usually found in Ehlers-Danlos syndrome (EDS). This suggests that SCAD is frequently associated with the dermal alterations seen in EDS.

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عنوان ژورنال:
  • Neurology

دوره 63 9  شماره 

صفحات  -

تاریخ انتشار 2004